Total colonic aganglionosis associated with interstitial deletion of the long arm of chromosome 10. Late diagnosis of hirschsprung s disease article pdf available in journal of coloproctology 53 may 2015 with 176 reads how we measure reads. Article pdf available january 2017 with 2,015 reads. Early recognition and surgical correction of hirschsprung disease protects affected infants from enterocolitis and debilitating constipation. Resultados funcionales en ninos tratados quirurgicamente con. The affected segment is of small caliber with proximal dilatation. Hirschsprung disease aganglionosis, colonic colonic aganglionosis megacolon, congenital aganglionosis, rectosigmoid colon aganglionosis, total colonic congenital megacolon. Dec 30, 2019 in 1886, harold hirschsprung first described hirschsprung disease as a cause of constipation in early infancy. Menor dolor, menor diseccion, no genera adherencias intraperitoneales, excelente resultado estetico. Introduction hirschsprung s disease hd is a malformation of the large intestine characterized by the absence of ganglion cells in submucosal and myenteric plexus, which produces a functional obstruction and dilatation proximal to the affected segment 1. Hirschsprungs disease was a cause of neonatal obstruction in 26 22. Chronic constipation, megacolon, hirschsprungs disease. Hirschsprungs disease as a rare cause of refractory.
1056 965 1024 236 684 1329 712 1084 882 26 1281 484 702 289 1028 36 162 354 749 1127 767 548 1295 1464 821 665 949 923 1358 681 1002 859 1252 31 854